Total Glucosidase IIβ Cell-Based Colorimetric ELISA Kit

  • Catalog No.：KA3542C
  • Applications：ELISA
  • Reactivity：Human;Mouse
    • Gene Name：
    • PRKCSH
    • Human Gene Id：
    • 5589
    • Human Swiss Prot No：
    • P14314
    • Mouse Swiss Prot No：
    • O08795
    • Storage Stability：
    • 2-8°C/6 months
    • Other Name：
    • Glucosidase 2 subunit beta (80K-H protein) (Glucosidase II subunit beta) (Protein kinase C substrate 60.1 kDa protein heavy chain) (PKCSH)
    • Detection Method：
    • Colorimetric
    • Background：
    • disease:Defects in PRKCSH are a cause of polycystic liver disease (PCLD) [MIM:174050]. PCLD is an autosomal dominant disorder and is characterized by the presence of multiple liver cysts of biliary epithelial origin. PCLD is a distinct clinical and genetic entity that can occur independently from autosomal dominant polycystic kidney disease (ADPKD) [MIM:173900], which in a considerable but uncertain proportion of cases is associated with hepatic cysts.,function:Regulatory subunit of glucosidase II.,pathway:Glycan metabolism; N-glycan metabolism.,similarity:Contains 1 PRKCSH domain.,similarity:Contains 2 EF-hand domains.,subunit:Heterodimer of a catalytic alpha subunit (GANAB) and a beta subunit (PRKCSH). Binds glycosylated PTPRC.,
    • Function：
    • intracellular signaling cascade, protein kinase cascade,
    • Subcellular Location：
    • Endoplasmic reticulum .

    Attributes

    • Code：
    • KA3542C
    • Size
    • 96 / well
    • Price$：
    • 330
    • Delivery：
    • 2024-12-10
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